Keywords
To read this article in full you will need to make a payment
Purchase one-time access:
Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online accessOne-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribers receive full online access to your subscription and archive of back issues up to and including 2002.
Content published before 2002 is available via pay-per-view purchase only.
Subscribe:
Subscribe to Clinics in Chest MedicineAlready a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
References
- A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto.J Clin Epidemiol. 1988; 41: 583-591
- Better nutritional status in early childhood is associated with improved clinical outcomes and survival in patients with cystic fibrosis.J Pediatr. 2013; 162: 530-535 e1
- Early life growth trajectories in cystic fibrosis are associated with pulmonary function at age 6 years.J Pediatr. 2015; 167: 1081-1088 e1
- Early-life height attainment in cystic fibrosis is associated with pulmonary function at age 6 years.Ann Am Thorac Soc. 2021; 18: 1335-1342
- Mortality in adults with cystic fibrosis requiring mechanical ventilation. cross-sectional analysis of nationwide events.Ann Am Thorac Soc. 2019; 16: 1017-1023
- A contemporary survival analysis of individuals with cystic fibrosis: a cohort study.Eur Respir J. 2015; 45: 670-679
- Gastrointestinal outcomes and confounders in cystic fibrosis.J Pediatr Gastroenterol Nutr. 2005; 41: 273-285
- Challenges with optimizing nutrition in cystic fibrosis.Expert Rev Respir Med. 2019; 13: 533-544
- Academy of nutrition and dietetics: 2020 cystic fibrosis evidence analysis center evidence-based nutrition practice guideline.J Acad Nutr Diet. 2021; 121: 1591-15636 e3
Saxby N, Painter C, Kench A, King S, Crowder T, van der Haak N, et al. Nutrition guidelines for cystic fibrosis in Australia, 2017 Australia and New Zealand. Bell S, editor, Sydney: Thoracic Society of Australia and New Zealand; 2017. Available from: https://www.thoracic.org.au/journal- publishing/area?command=record&id=46.
- ESPEN-ESPGHAN-ECFS guidelines on nutrition care for infants, children, and adults with cystic fibrosis.Clin Nutr. 2016; 35: 557-577
- Age-specific guidelines.(Available at:)
- Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study.Lancet Respir Med. 2016; 4: 107-115
- Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation.Am J Respir Crit Care Med. 2013; 187: 1219-1225
- A CFTR potentiator in patients with cystic fibrosis and the G551D mutation.N Engl J Med. 2011; 365: 1663-1672
- Growth in prepubertal children with cystic fibrosis treated with ivacaftor.Pediatrics. 2017; 139
- Combination CFTR modulator therapy in children and adults with cystic fibrosis.Lancet Respir Med. 2021; 9: 677-679
- Nutritional status improved in cystic fibrosis patients with the G551D mutation after treatment with ivacaftor.Dig Dis Sci. 2016; 61: 198-207
- Energy balance and mechanisms of weight gain with ivacaftor treatment of cystic fibrosis gating mutations.J Pediatr. 2018; 201: 229-237 e4
- Impact of CFTR modulation on intestinal pH, motility, and clinical outcomes in patients with cystic fibrosis and the G551D mutation.Clin Transl Gastroenterol. 2017; 8: e81
- Ivacaftor treatment of cystic fibrosis in children aged 12 to <24 months and with a CFTR gating mutation (ARRIVAL): a phase 3 single-arm study.Lancet Respir Med. 2018; 6: 545-553
- Safety and efficacy of elexacaftor/tezacaftor/ivacaftor for 24 weeks or longer in people with cystic fibrosis and one or more f508del alleles: interim results of an open-label phase 3 clinical trial.Am J Respir Crit Care Med. 2021; 203: 381-385
- Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.Lancet. 2019; 394: 1940-1948
- Clinical effectiveness of elexacaftor/tezacftor/ivacaftor in people with cystic fibrosis.Am J Respir Crit Care Med. 2021; 205: 529-539
- Cystic Fibrosis Foundation .Cystic Fibrosis Foundation Patient Registry 2020 Annual Data Report Bethesda, Maryland ©2021 Cystic Fibrosis Foundation.
- Highlights from the nutrition guidelines for cystic fibrosis in Australia and New Zealand.J Cyst Fibros. 2020; 19: 16-25
- Fat-free mass depletion in cystic fibrosis: associated with lung disease severity but poorly detected by body mass index.Nutrition. 2010; 26: 753-759
- Association between body composition and pulmonary function in children and young people with cystic fibrosis.Nutrition. 2018; 48: 73-76
- Tools and methods used for the assessment of body composition in patients with cystic fibrosis: a systematic review.Nutr Clin Pract. 2019; 34: 701-714
- Association between fat-free mass and pulmonary function in patients with cystic fibrosis: a narrative review.Nutr Clin Pract. 2019; 34: 715-727
- Effects of diagnosis by newborn screening for cystic fibrosis on weight and length in the first year of life.JAMA Pediatr. 2017; 171: 546-554
- Prevalence and factors associated with overweight and obesity in adults with cystic fibrosis: a single-center analysis.J Cyst Fibros. 2020; 19: 139-145
- Nutritional status and lung function in children with pancreatic-sufficient cystic fibrosis.J Cyst Fibros. 2021; S1569-1993: 02173-02181
- Obesity in cystic fibrosis.J Clin Transl Endocrinol. 2021; 26: 100276
- Body composition and lung function in cystic fibrosis and their association with adiposity and normal-weight obesity.Nutrition. 2016; 32: 447-452
- Abnormal lipid concentrations in cystic fibrosis.Am J Clin Nutr. 2002; 75: 1005-1011
- Prevalence of dyslipidemia in adults with cystic fibrosis.J Cyst Fibros. 2010; 9: 24-28
- LDL-cholesterol and insulin are independently associated with body mass index in adult cystic fibrosis patients.J Cyst Fibros. 2012; 11: 393-397
- Cardiovascular complications in cystic fibrosis: a review of the literature.J Cyst Fibros. 2021; 21: 18-25
- Preclinical atherosclerosis in cystic fibrosis: two distinct presentations are related to pancreatic status.J Cyst Fibros. 2021; 21: 26-33
- Dietary macronutrient distribution and nutrition outcomes in persons with cystic fibrosis: an evidence analysis center systematic review.J Acad Nutr Diet. 2021; 121: 1574-15790 e3
- Clinical Practice Guidelines on G, et al. Evidence-based practice recommendations for nutrition-related management of children and adults with cystic fibrosis and pancreatic insufficiency: results of a systematic review.J Am Diet Assoc. 2008; 108: 832-839
- Visceral adipose tissue is associated with poor diet quality and higher fasting glucose in adults with cystic fibrosis.J Cyst Fibros. 2019; 18: 430-435
- Dietary intake of energy-dense, nutrient-poor and nutrient-dense food sources in children with cystic fibrosis.J Cyst Fibros. 2018; 17: 804-810
- The relative contribution of food groups to macronutrient intake in children with cystic fibrosis: a European multicenter assessment.J Acad Nutr Diet. 2019; 119: 1305-1319
- Adherence to dietary recommendations, nutrient intake adequacy and diet quality among pediatric cystic fibrosis patients: results from the greecf study.Nutrients. 2020; 12: 3126
- Association between dietary factors and mortality from heart disease, stroke, and type 2 diabetes in the United States.JAMA. 2017; 317: 912-924
- Physical activity in children and adolescents with cystic fibrosis: a systematic review and meta-analysis.Pediatr Pulmonol. 2020; 55: 2863-2876
- Physical activity and associations with clinical outcome measures in adults with cystic fibrosis; a systematic review.J Cyst Fibros. 2019; 18: 590-601
- The effect of an intensive residential rehabilitation program on body composition in patients with cystic fibrosis.Eur J Pediatr. 2021; 180: 1981-1985
- Improvement in body composition following a supervised exercise-training program of adult patients with cystic fibrosis.Respir Med Res. 2019; 75: 5-9
- Enteral tube feeding for individuals with cystic fibrosis: cystic Fibrosis Foundation evidence-informed guidelines.J Cyst Fibros. 2016; 15: 724-735
- Enteral tube feeding for cystic fibrosis.Cochrane Database Syst Rev. 2019; 7: CD001198
- Enzyme cheat sheet.(Available at:)
- Effect of an organized lipid matrix on lipid absorption and clinical outcomes in patients with cystic fibrosis.J Pediatr. 2002; 141: 178-185
- Increased fat absorption from enteral formula through an in-line digestive cartridge in patients with cystic fibrosis.J Pediatr Gastroenterol Nutr. 2017; 65: 97-101
- Absorption and safety with sustained use of RELiZORB evaluation (ASSURE) study in patients with cystic fibrosis receiving enteral feeding.J Pediatr Gastroenterol Nutr. 2018; 67: 527-532
- Announces FDA labeling revision approval for PERTZYE(R) (pancrelipase).(Available at:)
- Maximal daily dose of pancreatic enzyme replacement therapy in infants with cystic fibrosis: a reconsideration.J Cyst Fibros. 2013; 12: 784-785
- Relationship of initial pancreatic enzyme replacement therapy dose with weight gain in infants with cystic fibrosis.J Pediatr Gastroenterol Nutr. 2018; 67: 520-526
- Pancreatic enzyme replacement therapy use in infants with cystic fibrosis diagnosed by newborn screening.J Pediatr Gastroenterol Nutr. 2018; 66: 657-663
- Cystic fibrosis, body composition, and health outcomes: a systematic review.Nutrition. 2018; 55-56: 131-139
- Cystic fibrosis bone disease treatment: current knowledge and future directions.J Cyst Fibros. 2019; 18: S56-S65
- Body composition, lung function, and prevalent and progressive bone deficits among adults with cystic fibrosis.Joint Bone Spine. 2016; 83: 207-211
- The effects of ivacaftor on bone density and microarchitecture in children and adults with cystic fibrosis.J Clin Endocrinol Metab. 2021; 106: e1248-e1261
- Epidemiology, pathophysiology, and prognostic implications of cystic fibrosis-related diabetes: a technical review.Diabetes Care. 2010; 33: 2677-2683
- Microalbuminuria in patients with cystic fibrosis.Diabetes Care. 2011; 34: 1526-1528
- Microvascular complications in cystic fibrosis-related diabetes.Diabetes Care. 2007; 30: 1056-1061
- Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society.Diabetes Care. 2010; 33: 2697-2708
- Cystic fibrosis related diabetes: nutrition and growth considerations.J Cyst Fibros. 2019; 18: S32-S37
- Dietary intake in cystic fibrosis and its role in glucose metabolism.Clin Nutr. 2020; 39: 2495-2500
- Fat-soluble vitamin deficiency in children and adolescents with cystic fibrosis.J Clin Pathol. 2014; 67: 605-608
- Relationship between fat-soluble vitamin supplementation and blood concentrations in adolescent and adult patients with cystic fibrosis.Nutr Clin Pract. 2014; 29: 491-497
- Consensus report on nutrition for pediatric patients with cystic fibrosis.J Pediatr Gastroenterol Nutr. 2002; 35: 246-259
- Update on fat-soluble vitamins in cystic fibrosis.Curr Opin Pulm Med. 2008; 14: 574-581
- Vitamin A and E deficiency and lung disease in infants with cystic fibrosis.J Paediatr Child Health. 2005; 41: 663-668
- Elevated vitamin A intake and serum retinol in preadolescent children with cystic fibrosis.Am J Clin Nutr. 2006; 84: 174-182
- Vitamin A intake and elevated serum retinol levels in children and young adults with cystic fibrosis.J Cyst Fibros. 2008; 7: 137-141
- Individualized vitamin A supplementation for patients with cystic fibrosis.Clin Nutr. 2013; 32: 805-810
- An update on the screening, diagnosis, management, and treatment of vitamin D deficiency in individuals with cystic fibrosis: evidence-based recommendations from the Cystic Fibrosis Foundation.J Clin Endocrinol Metab. 2012; 97: 1082-1093
- How an increased intake of alpha-tocopherol can suppress the bioavailability of gamma-tocopherol.Nutr Rev. 2006; 64: 295-299
- Vitamin E status and its determinants in patients with cystic fibrosis.Adv Med Sci. 2018; 63: 341-346
- Vitamin K: the effect on health beyond coagulation - an overview.Food Nutr Res. 2012; 56: 1https://doi.org/10.3402/fnr.v56i0.5329
- Understanding the relationship between sweat chloride and lung function in cystic fibrosis.Chest. 2013; 144: 1418
- Precision nutrition and the microbiome part II: potential opportunities and pathways to commercialisation.Nutrients. 2019; 11: 1468
- Precision nutrition and the microbiome, part I: current state of the science.Nutrients. 2019; 11: 923
- Gut microbiota in children with cystic fibrosis: a taxonomic and functional dysbiosis.Sci Rep. 2019; 9: 18593
- Fecal dysbiosis in infants with cystic fibrosis is associated with early linear growth failure.Nat Med. 2020; 26: 215-221
- Influence of acid blockade on the aerodigestive tract microbiome in children with cystic fibrosis.J Pediatr Gastroenterol Nutr. 2021; 72: 520-527
- Probiotics for people with cystic fibrosis.Cochrane Database Syst Rev. 2020; 1: CD012949
- ECFS best practice guidelines: the 2018 revision.J Cyst Fibros. 2018; 17: 153-178
- Clinical practice guidelines from the cystic fibrosis foundation for preschoolers with cystic fibrosis.Pediatrics. 2016; 137: e20151784
- Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening.J Cyst Fibros. 2010; 9: 323-329
- Cystic fibrosis foundation practice guidelines for the management of infants with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome during the first two years of life and beyond.J Pediatr. 2009; 155: S106-S116
- Guidelines for the management of pregnancy in women with cystic fibrosis.J Cyst Fibros. 2008; 7: S2-S32
- Cystic fibrosis adult care: consensus conference report.Chest. 2004; 125: 1S-39S
Article info
Identification
Copyright
© 2022 Elsevier Inc. All rights reserved.
